Utano, Zvirwere uye Conditions
Myasthenia gravis: chii? Zvinokonzera, Zviratidzo neMarapirwo Nzira
Myasthenia rinonzi chirwere icho pamwe kwakawedzera tsandanyama simba. Zvakafanana chirwere yakatanga kurondedzerwa muna 1672. Maererano nenhamba, chirwere ichi hakuitiki kazhinji. Kunyange zvakadaro, vanhu vakawanda vari vanofarira mibvunzo pamusoro nei pane munhurume, chii uye chii nezviratidzo zvaitevera. Pashure pezvose, mangwanani chirwere zvinoenderana zvaiitwa uye kunaka kwoupenyu munhu anorwara.
Myasthenia gravis - chii? The zvinokonzera chirwere
Kana zvose zvinoitika, acetylcholine pamusoro excitation anopinda synaptic mumukaha, izvo anoita dzakananga receptors mu tsandanyama Kamudzira - Saka dzinovhurika uye rutapudzo kuti tsandanyama fibers. Asi vacheche, mashandiro uyu kwemashoko etsinga chido raputsika.
Pakarepo zvinokosha kuziva kuti myasthenia gravis - nemagene chirwere. Uye nhasi akasarudza govera zviviri zvinokosha siyana ayo kukura. Mune zvimwe zviitiko, kukundikana nokubata etsinga zvairatidza inobatanidzwa nokuvhiringidzirwa kunowanzoitika kushanda hypothalamus. Chimwe chikonzero zvinowanzovapo chirwere chiri autoimmune lesion pamusoro thymus shwanu, iyo inotungamirira zvinoderedza mari synthesized acetylcholine.
Pane inonzi neonatal myasthenia gravis. Chii? Ichi chimiro chirwere kunoitika vachangoberekwa kana vanamai vavo vanotambura kusagadzikana neuromuscular conduction.
Zviratidzo zviri chirwere anogona kuratidza sezvo mumazuva okutanga pashure pokuberekwa, uye mune zvimwe munhu akura. Pane zvimwe zvinhu zvinokonzera njodzi kuti aigona kuti kukura myasthenia gravis. Zvikonzero kurwisa kuti tsandanyama simba kunogona nokuda kuzvidya mwoyo, huta kushushikana, zvekare zvirwere uye zvinetso zviri zvirwere.
The chikuru zviratidzo myasthenia gravis
Sezvambotaurwa, chikuru chepfungwa chirwere ndiye tsandanyama simba. Mangwanani, varwere kazhinji kunzwa zvakakwana chakaipa. Asi maawa mashoma ari skeletal tsandanyama kuneta uye kumisa kushanda, kusvikira apedzise dzomuviri. Mushure achizorora anogona kuderedza akapora.
Zvichienderana boka kwakakanganisa utano hwake rakakamurwa huru nhatu siyana chirwere:
- Kazhinji, chirwere kunokanganisa tsandanyama, ayo innervated ne cranial tsinga. Uye chikuru chikabviswa hazvisi ptosis. Kana munhu anogona kuzorora zvakakwana svinudzai meso enyu, zvino pashure pemaawa mashomanana, pane zvishoma nezvishoma vachirembedza okumusoro kukotsira.
- Panewo bulbar myasthenia gravis. Chii? chirwere ichi pamwe pakaputsika etsinga chido kupfuudzwa kuna tsandanyama, izvo basa iri kumedza, kutsenga uye dzimwe kwendangariro. Varwere vanhu vane matambudziko nokudya, uyewo zvishoma nezvishoma kuchinja inzwi, kusvikira rakwo kunyangarika.
- Kazhinji generalized chimiro maperembudzi chirwere, umo ziso tsandanyama vanotanga sei, ipapo muitiro rinobva pamutsipa, okumusoro kuviri, uye zvichingodaro. D.
Nzira Mabatirwo myasthenia
Zvinokosha kucherechedza kuti myasthenia chirwere gravis ngozi kwazvo uye kunoda kutarisirwa unyanzvi. Chokwadi ndechokuti chirwere ichi kunoratidzwa vanonzi nematambudziko, ayo achiperekedzwa kwenguva pfupi kuoma kufema tsandanyama, uye ichi ndicho zvakananga upenyu.
The chete zvinobudirira kurapa ndiyo yaitonga zvinodhaka zvine acetylcholinesterase - a "Proserpine" uye "Kalimin". kurapa kwakadaro okupedzisira kwemakore, uye dose zvokurapa zviri dzichichinja zvichienderana mamiriro uye mwero pakukura chirwere. Kana myasthenia gravis yakatanga tikafunga bundu iri thymus shwanu, kuvhiya rinoitwa kubvisa muviri.
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