Hirschsprung chirwere

chirwere Hirschsprung zvinoreva kuti malformation pamusoro rworuboshwe hafu muura. It kunoratidzwa kusavapo ganglion masero ari submucosal uye intramuscular plexus. chirwere Hirschsprung raMwari rinowanikwa mune vana nhamba 1: 5000 nyaya. In kuyaruka, inowanikwa ndoda kakawanda. Boys kutambura kashanu kakawanda kupfuura vasikana. Nokuti ichi pathological ezvinhu dzinoratidzwa rwapedyo nhaka. Mune zvimwe zviitiko, maperembudzi chokuita nechitarisiko pamusoro Down syndrome. In akura chirwere Hirschsprung kuti kunoitika apo mamiriro localization ari anorectal nharaunda. In Muzviitiko zvakaipisisa, zvinogona kuparadzira kune distal ura diki.

Mune pathogenesis chirwere inoita basa rinokosha kushaya pokudzora parasympathetic weboka tsinga. Mugumisiro ichi ndicho kunonoka rekambani sphincter kutandara mugaranhoko, iyo inosvitsa zvachose zvinoderedza spastic, chinovhiringidza pamusoro peristalsis, nokuwedzera hypertrophy. Akaora hosha kuratidza mamiriro rinozivikanwa sezvo megacolon.

chirwere Hirschsprung kunogona kuitika nenzira ndanyarara hangu, decompensated subcompensated uye chimiro. The kwokuomerwa ari pathological ezvinhu zvinoenderana anglionarnogo mugove kureba. Decompensated chimiro kunoratidzwa kwazvo zviratidzo ileus.

Maitiro zviri chirwere vari kurwadziwa kwazvo, bloating, kutinhira dumbu, kupatira. Kunonoka rwecheya ane chirwere kosi (dzimwe nguva kusvika mwedzi). Bloating zvakare kuramba kuchiitwa chirwere, rinorema uye zvinogona kukonzera dambudziko chinofema mwana. Bloating unogara kunyange pashure bowel sangano achibatsirwa enemas. mugumisiro wayo anogona kunzi nechitarisiko kurwadziwa kwazvo. The chikuru Zviratidzo chirwere vari zvakabatanidzwa kuda kurutsa, kurutsa, utera, kudya kudzikira. Matambudziko ichi pathological ezvinhu vari kupererwa, deformation edzinza pamakona. Kuvapo kuzvimba, ulceration, goiter kungamutsa kuramba manyoka anokonzera kuneta, collaptoid mamiriro.

Chirwere Hirschsprung chirwere chinotanga kutarisana vaongo-. Nemuumbi kuwedzera mudumbu nokuda dzose pakazvimba, peristaltic sunga iri kukanganiswa ura, gobvu chetsoka. Kuchinja marwadzo ari mumagaro sphincter vagara vandifungira digitaalinen kuzviongorora. Fluoroscopy wakarurama inopa akarurama chaizvo zvabuda. Kunoonekwa shanduko intestinal muenzaniso nokuda pamberi zvinokosha rakawanda magasi anokonzera mhingaidzo. Mune dzimwe nzira paku inoshandiswa nechirwere ose pathological ezvinhu vari colonoscopy, barium enema. The yokupedzisira inoshandiswa kuona kukura uye localization pamusoro constriction dhayamita suprastenoticheskoy muura nharaunda.

Kuti asimbise nechirwere inoshandiswa transanal biopsy. Kuderedza neuronal ganglia intermuscular plexus chinhu chinowanika inobvumirana Hirschsprung chirwere. Munguva oparesheni, nzira iyi inobatsira kuona padanho resection.

Pakurapa chirwere wehurumende kunoenderana kwokuomerwa kwayo kosi. Ndanyarara hangu siyana zvinogona kubviswa nokuda kuchinja nzira yokurapa, mune zvimwe zviitiko zvinoda kukurumidzirwa kuvhiya kupindira, ndiko kumanikidza kolonostomy, achibvisa aganglionarnoy nharaunda, decompensated, overextension huru ura. Rufu pashure vakaperekedza kurapwa anouya kusvika mana muzana.