UtanoZvirwere uye Conditions

Chii chinosiyanisa Brugada chirwere?

Maererano nenyanzvi, Brugada chirwere iri rakava muboka chinonyanya mwoyo chirwere zvemagetsi rurefu chaizvo mukana vanonzi "kufirwa aritimicheskoy". chirwere ichi kazhinji achiperekedzwa refu kakawanda ventricular fibrillation, uye ST chidimbu pakakwirira.

epidemiology

Zvinofungidzirwa kuti Brugada chirwere iri nechirwere kakawanda 4 anenge 12% vose huripo zviitiko kufirwa kubva siyana zvirwere mwoyo. Maererano nenyanzvi, kunyanya chirwere ichi rinowanika 10 nguva kakawanda muna hono hafu yevagari.

pakarepo zvikonzero

Panguva iyoyo, mashoko okupedzisira zvinokonzera chirwere ichi vasiri aizvinzwisisa. Zvisinei, vanachiremba vanodavira kuti kana Gene kunotouraya vanonzi "yavaibvisa mugero" ari SCN5A mikana inowirirana kukura chirwere.

Brugada chirwere: ECG zviratidzo

Chekutanga zvinofanira kucherechedzwa kuti chikuru zviratidzo kazhinji dzinoitika vanhu pashure pemakore makumi mana. Saka, vanachiremba vane zvinhu zvinotevera kuti vari anoratidza pamberi chirwere:

  • tichibatwa kufema zvirwere kunyanya usiku;
  • syncope;
  • polymorphic ventricular tachycardia;
  • Zvikamu zviri ventricular fibrillation.

mabatiro

In chirwere akadai Brugada urwere, ECG achinyanya inoratidza zvaibvira yakatsauka kubva dzose utano murwere. Somunhu rokutanga kurapwa nyanzvi kazhinji mishonga mushonga "quinidine" uye dzimwe nzira, kusanganisira zvinodhaka "Isoproterenol". Achitaura vapedzisira, zviri sechinhu inobudirira chaizvo mushonga kuti anokwanisa chaizvoizvo achapwanya "zvemagetsi dutu" kuti unowanikwa varwere pamwe chirwere usiku. Sezvo mukuru nzira yokudzivirirwa vanonzi "rufu kusingatarisirwi 'murwere, vanachiremba dzinorumbidza kugadzwa cardioverter-defibrillator. Zvinofanira kucherechedzwa kuti kana chirwere Brugada urwere, pasina kwokunze zvinoratidza chirwere vanofanira achiri kugara muonekwe unyanzvi. Zvisinei, pamusoro akarondedzera muchibereko cardioverter-defibrillator mune iyi haisi kuzvireva.

matanho

Panguva iyoyo, Brugada chirwere kunokwanisa kuonekwa nekaupenyu kashoma. Sezvo matanho , vanachiremba zano zvakasimba narwo dzose kuongorora. Zvinoreva kuita zvikuru Diagnostics zvose, kusanganisira unonzi, electrocardiograph, miedzo ropa uye weti nemiedzo. The ndechokuti zviri pamusoro zvinoriumba izvi uye anogona kutonga pamberi matambudziko pamuviri. Cherechedza kuti kuvapo pedyo "hama" nechirwere zviri kwairayirwa kuita zvikuru zvakawanda kuongororwa, izvo zvinozoita rinoreva tsanangudzo vanonzi "chawo pangozi" uyewo haizopereri richiona murwere kwenguva refu, kuchitsamira pamunhu utano zviratidzi . Chete nenzira iyi, sezvo zvinoratidza, unogona kudzivisa rufu, kuti zvinobvira nekutambira matambudziko, uye kudzivirira zvirwere kunyange mangwanani zvikuru nzendo kukura. Stay utano!

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