Lou Gehrig kuti syndrome. How kubata chirwere Charcot?

Charcot kuti chirwere - chii uye sei kuratidza? Kuti isu chose kuratidzwa munyaya ino.

Description of chirwere

Charcot Syndrome (kana inoratidza claudication) chirwere dzinoratidzwa chitarisiko uyewo enhancement kurwadziwa uye kusimba rezasi migumo panguva kufamba. Matafura kwakadaro kazhinji kuti murwere kumisa, nokuti zviratidzo chete ainzi anenge havatsvaki. Kakawanda kurambwa uku vanhu kupesvedzera somugumisiro:

• Kushapira doro uye fodya;
• remesa;
• BP remafuta akawandisa mumatunhu;
• nhodzera, uye zvichingodaro.

Huru Zviratidzo

Charcot kuti chirwere - iri chaizvo chinorwadza mamiriro iri kukonzera murwere kusanzwa uye yekudyidzana kunokanganisa huri upenyu. Akarambwawo uyu munhu kazhinji anonyunyuta nokuneta, uyewo kusanzwa uye marwadzo makumbo apo tichifamba, kunyanya mune magaro uye mhuru tsandanyama. Pane zviitiko apo marwadzo vemunyika mune tsandanyama dzomuviri womunhu pazvidya uye muchiuno. Sezvo varwere vane chirwere kuti Charcot nehosha pamwe kunodzikira uye simba pakarepo pashure zororei.

In chirwere chakadaro distal dzakaderera ehomwe murwere vanowanzotambura akacherechedza trophic uye vegetative-vascular zvinetso (semuenzaniso, akrozianoz, tsoka inotonhora, marbling ganda uye chinopedza kuchinja, kushayikwa kupomba ari arteries norutsoka uye neronda rinonyenga pamusoro minwe, izvo kazhinji rinokoka proximally mirayiridzo).

Uyezve, Lou Gehrig kuti chirwere kunoratidzwa chinopedza uye dystrophic kuchinja mapfupa uye mapfundo (hypertrophy kwemunhu zvikamu, ari degeneration kuti shwashwa, mapfupa sequestrations, osteophytes, intraarticular uye kwatangwa mitswe mapfupa refu). Mukuwedzera, laxity uye kuderedzwa aikanganiswa pakati mapfundo yekudyidzana kunowedzera ngozi yokubatwa yaizoitika makuvaro.

zvinokonzera

Charcot kuti chirwere - chirwere kunokonzerwa pokukundwa gumbo arteries (thromboangiitis, obliterans atherosclerosis, peripheral chimiro nonspecific aortoarteritis uye zvichingodaro.). Marwadzo murwere kuitika nokuda kukwana ropa riyerere kuti tsandanyama rinenge repasi wamativi. Uyewo, chirwere kungaguma compression pamusoro Kaudha equina mu musana stenosis, kanenge - somugumisiro musana ischemia ari arteriovenous malformation, kana atherosclerosis yacho yeropa.

pakurapa chirwere

Zvipatara Intermittent claudication Nde tsime zvakananga pakurapa chirwere, kureva arteries. Kazhinji, mune zviitiko zvakadaro vanachiremba angarayira varwere vavo kupa tsika dzose dzakaipa, uremu uye kutevera vaitofanira kudya. Varwere vari anopiwawo rinokosha akagadzirwa muviri, kuti aizokunda zviratidzo chirwere.

Kana kuchinja nzira kurapwa, ipapo anosanganisira kugamuchira mishonga siyana. Zvavakaita anopa unonyaradza marwadzo uye vasodilator maturo. Uyewo, mishonga agents anobatsira yakaderera remafuta akawandisa muropa uye rayo dilution.

In chenjera kudiwa kuvhiya kupindira kushandiswa kwacho iyo anowedzera kuti tsinga lumen nokusuma mariri rinokosha anobudisa mushonga zvishoma nezvishoma.

Syndrome, Charcot-Marie-Tooth chirwere

kutsauka ichi chinomirira boka nhaka zvirwere, ayo kuburikidza degeneration pamusoro peripheral tsinga fibers inozivikanwa. Zvinofanira kucherechedzwa kuti dzakasiyana siyana inonzi urwere zvinogona kwakavakirwa siyana vaberekwe vakaremara. Vazhinji zvirwere izvi zviri nhaka ive autosomal kureva mashandiro. Zvisinei, pari zvino kuzivikanwa uye embodiments zvirwere chokuita adhesion pamusoro X chromosome.

In chirwere kwakadaro, Charcot-Marie urwere, mune murwere sei musana uye peripheral tsinga. Zvichienderana dzakananga nemagene akaremara vanhu inogona kuumbwa axonal kana demyelinating neuropathy.

Kakawanda kumiririrwa yakatsauka kachitanga kuyaruka kana kuyaruka. Zviratidzo boka iri chirwere pakupedzisira yakakura, uye hosha mberi apo anowanikwa kwakanaka dhigirii yokuremara, cherufu.

Zviratidzo kurambwa

chirwere ichi anotanga kubuda kubva distal tsandanyama atrophy uye neutera gumbo munyama. Nokufamba kwenguva, akaremara tsoka uye zvigunwe makuru uye hammertoes. In vana vane chirwere ichi chinenge nguva dzose kuona kunonoka kwomuviri.

Mabatirwo enhaka zvirwere

Dzakananga kurapa pane pathological ezvinhu akadaro haako. Zvisinei, kuvandudza utano varwere, vanachiremba kazhinji mishonga physiotherapy uye Occupational kurapa. Uyezve, varwere chirwere ichi vari zvikuru kushandiswa zvemarudzi ose yezvokurapa namano kuti kubvumira kubvisa marwadzo zviratidzo. Somuenzaniso, apo chidzitiro rutsoka kushandisa vachibatsira chibooreso muedzo shank uye zvichingodaro. Uyewo ine hwakanyatsorwisa guru ukoshi Genetic Counseling.

Von Willebrand chirwere

Zvinofanira kucherechedzwa kuti kune nhaka zvirwere zvinosanganisira kwete chete Charcot Syndrome. chirwere Von Willebrand hunogonawo pachishandiswa pedyo nehama.

Sezvo chikazozikamwa, nokutsauka chinomirirwa rakajairika nhaka zvinetso, zvichitungamirira nokuvhiringidzirwa ropa coagulation kana pakugwamba muitiro. Zvisinei, kazhinji hosha rikaitika mararamiro somugumisiro nezvimwe zvirwere (kureva kuwana chimiro).

chirwere zviratidzo

Mukana ropa kana kutsauka kwakadaro yakasiyana zvichienderana rudzi chirwere. The chikuru zviri ichi enhaka rebipolar zviri idzokororo nosebleeds, chisingapembedzwi kupwanywa uye kupwanywa, ropa matadza, uye zvichingodaro. Vakadzi vanogona kuva rinorema kumwedzi, uye pakuzvarwa mukana yokurasikirwa yakawanda ropa.

pakurapa chirwere

Varwere chirwere ichi hapana kurapa zvakakodzera, asi mukana wokunzwa ropa vagara kusimudzirwa. Saka, murwere inogona kurumbidzwa kuti nezvinodhaka izvo kuderedza pachena chiratidzo chacho. Kana murwere yakarongerwa kuita kuvhiyiwa, chiremba anofanira kumushandisira chokudzivirira kurapwa.