Klippel-Trenaunay chirwere: photo, zviratidzo, kurapwa

More zvirwere muzvizhinji kuumbwa embryo kumwedzi. Naizvozvo, kuti kukanganisa kukura kwavo asingagoni nguva dzose. Pashure pezvose, dzakawanda abnormalities aya chirwere chete pashure pokuberekwa kwomwana. Uye vamwe zvikuru gare gare. Mumwe masero zvirwere inofanira kusanganisira Klippel-Trenaunay chirwere. The chirwere sezvayakawanikwa mukutanga remakore rechi20. Izvi zvakabatanidzwa chidzoke ane Sayenzi genetics. Kazhinji chirwere muvamwe varume. Zvisinei, zviri kuwanikwa pakati hadzi vanogara. Zvokurwara anonzi vachiberekwa vascular zvirwere.

urwere, Klippel-Trenaunay Description

Klippel-Trenaunay chirwere anoonekwa isingawanzowanikwi nemagene urema. Kufungidzira kukura zvokurwara ichi kwakaoma zvisingaiti, nekuti ndiko kuremara kushoma uye haina chirwere panguva yepamuviri. Zvisinei, mune zvimwe zviitiko, chirwere chinogona vanofungidzirwa Klippel-Trenaunay. The chirwere zvinoreva nechirwere chaunoberekwa unacho. Naizvozvo, kutodza pachisara kunofanira pasi vakadzi vane pamuviri mumhuri umo nyaya chirwere ichi chakaitika. Chimwe zita nokuti chirwere - hypertrophic hemangiectasia. The kunotoda mufananidzo Klippel-Trenaunay chirwere zvinosanganisira zviratidzo zvikuru zvitatu:

1. Varicose mutsinga.
2. Chimiro zera makwapa ganda.
3. Kuchinja upamhi uye urefu njodzi richiripo.

Mune zvimwe zviitiko skeletal uye akapfava zvinyama hypertrophy yaiitwa. Kazhinji zvokurwara dzinoratidzwa mberi kosi. The fungidziro kunobva kwokuomerwa vascular kuchinja. Kunyange zvazvo mhaka chirwere hazvigoni kubviswa, kuchirapa matanho kubatsira kuvandudza upenyu murwere. Vanhu vanotambura nezvirwere izvi basa akaremara.

Zvinokonzera Klippel-Trenaunay urwere

Nokuda kwechimwewo chikonzero, pane chirwere Klippel-Trenaunay? The chirwere kukura somugumisiro nemagene urema. anomaly Izvi chinopfuudzwa ari autosomal kureva nhaka mhando. Izvi zvinoreva kuti kana pane yakadaro majini akaremara rimwe vabereki, pane mukana mukuru chirwere ari mwana 50%. Uyewo, chirwere chinogona kuburikidza chizvarwa chimwe, kuti ndiye - kubva navanasekuru. Panyaya iyi, mukana ndiyo 25%.

Kufanana zvose nemagene abnormalities, vascular zvikanganiso kuva panguva fetus tishu bogmærke. Zvinogona kukanganisa kukuvadza. Izvi zvinosanganisira zvinhu zvakadai:

1. Psychological kusanzwa yokutanga shoma vhiki pamuviri.
2. Zvirwere zvinotapuriranwa. Zvikuru vari chisingaperi nemavhairasi maronda muviri.
3. Kushandisa zvinodhaka teratogenic ehupfumi.
4. Rubvumo mishonga asati pamuviri uye panguva yepamuviri.
5. Kusvuta uye chidhakwa.
6. Kusvibiswa dzedenga zvine chepfu, nemwaranzi.

Zvose izvi zvinhu zvinogona kukonzera kuchinja nomuviri vakadzi mwana asati aberekwa. Ndivo kunyanya ngozi iri tanga pamuviri. Mushure anomalies siyana zvinogona zvakapararira munyika iyi.

Mashandiro chirwere

Sei pane vascular kuchinja chirwere Klippel-Trenaunay? The chirwere kunoratidza Zviratidzo venous zvirwere. The mashandiro kuti kukura zvokurwara kuburikidza rakavhara water drainage ropa apasi kumigumo. Izvi imhaka yokuti venous lumen ari kujekesa, pane compression kuti mudziyo arterial bazi, hypertrophied tsandanyama, residual embryo tishu. Nokuda kuti kutyorwa kuri water drainage ropa pane neBP. Vienna ari zvishoma thinned, pachena kuti kukuvara. Uyezve, kwakakanganiswa mudzimu vharuvhu midziyo. Nokuda ropa stasis muzvidimbu inotanga hypertrophy. Nokuda kurega kunotanga akatambura trophic ushande. Naizvozvo, zvinyama pachena kuti ischemia. Mazhinji kunetswa ropa wedzerai kunotungamirira kuoma dzimwe nhengo dzomuviri. Soft zvinyama hypertrophy kunoitika hyperemia uye edema. Mune zvimwe zviitiko, zviri pasi kushandura uye mapfupa. Naizvozvo dzinoshamiswa rimwe gumbo murege chete kuwedzera yakafara, asi urebese.

Klippel Trenaunay Syndrome-: Zviratidzo

Pakazosvika kuratidzwa Klippel-Trenaunay chirwere zvinosanganisira kuchinja kwete chete pane chikamu venous ezvinhu, asi zvimwe zvikanganiso. Pasinei chokwadi kuti vachiberekwa abnormality, zviratidzo zvokutanga kuonekwe mu kuyaruka kana wakura. Nokudaro, kurapwa zvinozonzi zvinosanganisira zvinotevera kutyorwa:

1. Dilation pamusoro zvachero gumbo mutsinga. Kunoratidza pathological kinking uye marwadzo pamwe mudziyo chaioneka chinoabatsira. Muzviitiko zvizhinji varicose mutsinga iri rokunze pechiso makumbo.
2. Kuwedzera uwandu richiripo. Kunowanzoguma anogumbura zviitiko. Nokuda ropa stasis kukanganiswa gumbo angava akasiyana chaizvo kubva utano richiripo. Kazhinji zviri hyperemic, thickened ganda.
3. Richiripo dzikawedzerwa. Hypertrophy anogona zvose makumbo nemaoko.
4. The pakuonekwa pigmented nevi paganda. Mune imwe nzira, idzodzo izvi vanonzi "echitema waini".

Uyewo, pamwe kuchiita chirwere kuonekwe trophic kuchinja. maronda zvikanganiso munogona vawirwa nenjodzi, izvo regai kuporesa kwenguva refu. Pakati pezvimwe abnormalities kusimukira zvokurwara ichi, pane polydactyly, kuvapo fused interconnected minwe kana zvigunwe.

How rokuongorora chirwere Klippel-Trenaunay?

Syndrome chirwere pamusoro Klippel-Trenaunay runowanzotaurwa yakavakirwa yokuora kuratidzwa. Zviratidzo zviri chirwere kuonekwa zvishoma nezvishoma. The chiratidzo chokutanga zvingava pakuonekwa "echitema waini" kana mutsinga. Kana Zviratidzo aya pamwe hypertrophy pamusoro pabazi pachena zvokuongorora: Klippel-Trenaunay syndrome. Photos of vanhu vanotambura nezvirwere ichi akafanana nomumwe. Vanogona kuonekwa mabhuku inopedzerwa zvisingawanzoitiki nemagene pathologies. Saka, vakawanda chirwere haisi nyore.

Kuwedzera zvekuchipatara data, akaita venography, ultrasonography repasi maoko nemakumbo, X-ray.

Klippel Trenaunay Syndrome-: nokurapa chirwere

kuvhiyiwa anoonekwa rakakura chiitiko zvokurapa. Bhuku kupindira iri pakutsvaga mwero vascular lesion. Kuwedzera lumen pamusoro tsinga stenting rinoitwa. Kana huru nzvimbo wokuparadzwa unobereka yokunzvenga mudziyo - vachiitsiva ane kudyara paIndaneti.

Kuti tikurire varicose yakatarwa skleroteropiya, Laser coagulation pamusoro mutsinga. Varwere vanenge chirwere ichi anofanira kupfeka compression andapeni.

urwere, Klippel-Trenaunay Prevention

Klippel-Trenaunay chirwere muna vacheche haawanzopiwi chirwere. Kazhinji iri kuona pakutanga kwemwedzi kana makore oupenyu. Kudzivirira chirwere, zvakakodzera kuzvidzivirira kubva zvinokonzerwa panguva yepamuviri. Chimwe chiyero chokudzivirira runoonekwa kuva majini kuzviongorora mudumbu pamberi Muzviitiko chirwere mumhuri.