Utano, Zvirwere uye Conditions
Autoimmune thrombocytopenia: Inokonzera, nechirwere, Treatment
Pakati zvirwere autoimmune hunhu, sezvarinokodzera vainyatsotarisirwa thrombocytopenia. Nokuti akati chirwere maitiro chepfungwa ndiye rutapudzo mukuwanda maplatelet - zvinokosha ropa coagulation. Vasingazivi chii - chinhu autoimmune thrombocytopenia, varwere vakawanda nehanya zviratidzo chirwere wokutanga, uye sei kazhinji zvinoita sokuti maturo. In mazhinji matanho pane ngozi nemamwe matambudziko kurufu, uye mikana kuti kunaya zvakakwana - zvishoma.
Ndechipi thrombocytopenia: tsanangudzo pfupi
The chirwere kunoratidzwa nekusagona muviri zvirwere kuziva pachake maplatelet ayo, iyo inotungamirira chokudzingwa yavo. Mhedzisiro yacho pathological kwacho kuri kugadzirwa antibodies vari chirwatata, izvo nokukurumidza kumhanya kunobatsira kubvisa muviri "wokumwe". Kakawanda, chirwere kunooneka pacharo muchando uye yechirimo. dzimwe nguva yakaderera azvipire maplatelet muropa vari kutaura non-masoja chimiro chirwere. Kana ichi, thrombocytopenia, rinowanikwa panyaya zvinooneka migumisiro pamusoro maplatelet.
Anoreva boka zvirwere kweropa gadziriro, kupererwa neropa iri Classified akasiyana-siyana oushumiri. Most kazhinji chirwere yakakamurwa kureba aibuda kupinda mhando mbiri - chakasimba uye chisingaperi. Zvikuru ngozi vanhu ndiyo mhando hosha wechipiri, sezvo rokudzorera kuipa platelet count anogona kutora mishoma, uye dzimwe nguva kwemakore. Kunewo imwe kupatsanura pakati thrombocytopenia, zvinobva hosha yechipiri kana chikuru - chirwere anokwanisa kuratidza dzavo kana kuitika tikafunga mamwe abnormalities pamuviri.
Propensity nechirwere, mapoka njodzi
Kuitika thrombocytopenia ngozi zvakaoma vaiwanzoti munhu yoga chikamu wevarwere. Asi dzose kuchinja zvakadini masero matsvuku mumuviri vakadzi unotipa kuzodana naka pabonde zvikuru kubatwa nechirwere.
Chii zvinokonzera chirwere ichi?
With chokwadi chakakwana vanoti sei chirwere ichi hazvibviri. Asi, pasinei ichi, nyanzvi vanowanzomuitira tabvumirana pamusoro autoimmune thrombocytopenia purpura - basa guru kukonzera chirwere chinoita majini nhaka. Nokuti chero zvikonzero, autoimmune thrombocytopenia dzinosanganisira:
- sema maitiro muviri (zvikurukuru kunyaradza, antibacterial uye zvinodhaka alkaloid zvinogona kukonzera kusachengeteka kukuru chimiro chirwere);
- Immune Deficiency, simba kutapata;
- kuwedzerwa ropa, mismatched ropa;
- chenjera renal kukundikana;
- chisingaperi nehepatitis mhando;
- scleroderma;
- lupus;
- leukemias;
- doro.
Zvimwe kutanga chirwere vanhu vakaberekwa vaine HIV. Zvikonzero nekuratidza chirwere chinogona kunzi metastasis mumuviri pamberi malignancy. The kuderera mumasero ropa kunotungamirira folic iine acid kushaikwa, vhitamini B12, kana overabundance nemwaranzi dzokupisa, ultraviolet chiedza.
The chikuru zviratidzo zvechirwere autoimmune chirwere kwemarudzi
Symptomatology mamirire nokuti autoimmune thrombocytopenia, mumwe murwere kunoratidzwa dzakasiyana. Zvinoitwa chirwere takatsunga, pakutanga kwezvose, zvinokonzera chirwere, yezvakaita chirwere.
- The panowanikwa ganda kupwanywa, kubuda ropa. Kusiyana zvavo mavanga dzepepuru makwapa varwere cherechedzai kakawanda rezasi maoko nemakumbo, mutumbi uye chiso uye miromo.
- Mazhinji ropa zvinetso nokuda zvinyama kuvimbika (pashure kubviswa mazino, ronda zvachero, akachekwa).
- Kuwedzera remuromo node nodes pamwe kuramba nefivha yakaderera-mugiredhi.
- Palpable zvakawanda zvive, kusimba makumbo, dzungu.
Ndezvipi zviratidzo vanofanira kuteerera?
Kwokutanga nechirwere thrombocytopenia, zvinova nyore kuti kurapa nayo. Somuenzaniso, varwere kashoma kuteerera zviratidzo zvakadai ropa matadza, zviduku rashes pamusoro muviri. Mukana wokufungisisa uye kuenda kuongorora zviri zvachose nyarara uye guru hematoma mumatenhere munyama kuti kuitika kuchangotanga kukuvara, uyewo kusarudzwa mutsvina yadzo uye weti pamwe ropa.
Platelet kushayiwa panguva yepamuviri: zvikonzero huru
Pamuviri uye autoimmune thrombocytopenia chiremba funga dzinopesana ezvokurapa. Vakadzi vakamirira replenishment, nhamba masero eropa, kunyange chakaipa kosi kunosiyana-siyana pamwe chinozikamwa kusiyana, saka chiremba anogona kunzi basa hwakadzama dzose richiona ropa ezvinhu. Kazhinji panguva pamuviri, nhamba maplatelet vakadzi ipfupi kuti Activate ari peripheral riparadzirwe, asi kuchinja kwakadaro havasi kudaro inokosha kukonzera zvakakomba kuvhiringidzika muviri anokosha. Nenzira, zvinokonzera zvirwere vanamai pamuviri Kazhinji:
- Zvokudya kukodzera uye kushaya zvokudya;
- BP kurasikirwa;
- simbi kushaikwa kupererwa neropa;
- kuderera rokuzvidzivirira.
How kuzvara mwana ane utano pamwe thrombocytopenia?
All izvi zvinoita kutungamirira kukudziri- yakaderera mwongo matsvuku masero. Uyezve, vakawanda maplatelet anobudiswa, ane mugari chimiro. Munyika pamuviri, mwana asati azvarwa pachena kuti ngozi zvikuru kukonzera womukati kubuda ropa.
Chirwere: sei kusiyanisa nezvimwe zvirwere?
Usati asimbise autoimmune thrombocytopenia pakutanga zvakakosha kusiyanisa pakati etiology pakati platelet kushaikwa wechokwadi, nekuti vakawanda zviratidzo vane zvakafanana nemamwe zvinetso zvakakomba mumuviri:
- kupererwa neropa;
- rinotevera hematological zvirwere;
- metastasis mu mumwongo;
- splenomegaly marudzi - zvirwere chirwatata;
- kwemakemikari anobudiswa zvirwere.
Muzviitiko zvizhinji nechirwere pakati autoimmune thrombocytopenia haakonzeri zvinetso, sezvo ari kuonekwa ari chirwere, siyana kurapwa uye mumarabhoritari kutsvakurudza nzira. Kakawanda, vanachiremba kusimbisa chirwere zvinogoneka Via:
- navanachiremba ropa ongororo;
- nemakemikari ropa ongororo;
- cytology;
- Mwongo histology.
How kurapa kushayikwa maplatelet?
The koshesa Kuwanda pacho, pakurapa autoimmune thrombocytopenia ndiyo hormone. Panguva kurapa chirwere murwere ushandiswe mushonga gormonsoderzhaschie vakawanda chiri "prednisolone" - munhu glucocorticosteroid, ari kunze komutemo uye kusingadzoreki kushandiswa rakatarisana panowanikwa nemishonga. Kugadzirira ibasa ari kupinda chiremba, iyewo anotarisira chipimo chemushonga: paavhareji "prednisolone" Ratidzai kunobva nhamba 1 Rine mamiririta por 1 kg muviri uremu. At mazhinji zvokukura chirwere nyanzvi angasarudza kuwedzera uwandu husingakuvadzi kanenge kaviri.
Glucocorticoids nekusimba pachavo mukurwisa autoimmune thrombocytopenia, asi kazhinji zvinodhaka kurapa hunopa symptomatic chaizvoizvo muchimiro zvokurwara yechipiri. Panyaya iyi, kazhinji chete dambudziko iri kuvhiyiwa. Nokubviswa chirwatata iri mushonga anonzi splenectomy. The oparesheni rinoitwa laparoscopically. Asati kuita zvakananga kupindira chipimo chemushonga kubata mahormone kuwedzera katatu nokusuma zvakananga kupinda tsinga. Pashure nokubviswa chirwatata mwero "Prednisolone" hakuiti kugumisa - mushonga kutora makore maviri.
Zvinoumba Mabatirwo thrombocytopenia
Kana matambudziko vavapo mukufamba kuvhiya Mabatirwo autoimmune thrombocytopenia, murwere dzakabatwa pamwe cytotoxic mishonga immunosuppressive chaitika. In pakurapa chakakomba siyana chirwere inosanganisirawo matanho kudzorera chakaipa ropa vhoriyamu kubudikidza kuisirwa anyatsoronga. Kuti tidzivise dzokororo kwechirwere chacho, murwere afuke nhoroondo Vachinyora nguva nenguva firimu kuti prophylactic zvinangwa.
In kwokutanga nzendo chirwere ikarapwa nokukurumidza uye zvinobudirira, kusunungurwa rinowanzoberekera pashure kushandiswa kwezvinodhaka kwemazuva anoverengeka. Zvisinei, kuti abolition mishonga anofanira chikwata pamwechete chiremba - murwere, as a mutemo, kushandisa zvinodhaka kusvikira kwokupedzisira mushonga.
kurapwa uye kudya vanhu
Kurarama autoimmune thrombocytopenia zvinogona uye zvavo mishonga. At mazhinji zvokukura chirwere kunyatsoshanda yavo pasi, asi Rakabatanidzwa akasarudzwa kurapwa mishonga nzira kazhinji zvinoratidza migumisiro yakanaka. Vandudza ropa ehurumende uye kubatsira kuwedzera platelet count:
- uchi;
- fruit;
- razibheri;
- kuti aizomupa ruva hudyu;
- yorukato muto;
- bhiti uye Birch muto.
Kana thrombocytopenia, murwere dzinofanira kudzokororwa uye madyiro. Pasinei kushaya dzakananga vanorumbidza maererano zvokudya, kudzivisa pave zvomukati ropa kunokosha kutsenga zvokudya, kwete kudya zvokudya zvakare inopisa, kusiya zvinhu zviri muchishungurudza kune mucous membranes ari nemudumbu.
Zvinoita kuti ndiporese zvokurwara: asi for kupora
Achatanda autoimmune thrombocytopenia zvikuru pakutsvaga chimiro zvokurwara. Somuenzaniso, chirwere chiri rikwanise chokutambudzika, kubata nyore chaizvo pane chirwere mhando chirwere. Mune zvimwe zviitiko, kupora kunoitika pasina kushandisa mishonga. In chisingaperi thrombocytopenia kufanoona wokupedzisira kupora rakaoma zvikuru. Panguva iyoyo pachinhu murwere hwomunhu uyewo nengozi richamuka kana inguva yokutsvaka kushandiswa rubatsiro uye kutanga kurapwa pasina zvichitungamirira pezviri ropa.
Fungidziro ré kuderedza platelet count pavarwere vane chirwere autoimmune fomu iri zvakakwana guru, sezvo kungakonzera zvinhu zvakasiyana-siyana - mupfungwa kuti mamiriro kuchinja kana kugamuchira gadziriro dzokurapa. Zvazvo kazhinji achiperekedzwa kwazvo, asi nokuti varwere izvi zvinoda kwoupenyu hwose pokudzora unyanzvi. Zvinokosha kucherechedza kuti mafungiro dzisina anoruramiswa zvirwere vanosonganirana chirwere ichi kweropa hurongwa. Somuenzaniso, murwere mikana apore kubva neleukemia kana mwongo metastases usingashandi.
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