UtanoZvirwere uye Conditions

Aplastic kupererwa neropa: zviratidzo. Chirwere uye vabatwe aplastic kupererwa neropa

Mazuvano pane yakawanda zvakasiyana siyana nezvirwere kuti chokuita zvakananga ropa. Chimwe chaizvozvi aplastic kupererwa neropa. Zviratidzo chirwere ichi kuonekwa pakarepo. Zvinoita kurapa chirwere? Ndezvipi matanho? Ndizvo nezvazvo uye zvichakufambirai munyaya ino.

tsananguro

Aplastic kupererwa neropa chirwere kubva hematopoietic ezvinhu, apo pane yakapinza kuderera kwenhamba masero eropa, asi hapana dzakajeka zviratidzo kenza. Maererano nenyanzvi, zvokurwara ichi kwava kushoma. Zvingakurwadza varume fair pabonde, kazhinji pashure pemakore 50. Kana akasiya untreated aplastic kupererwa neropa kazhinji zvinouraya.

zvigadziriswe zvirwere kukura

Zvinozivikanwa kuti paumbwe ropa riri kuitwa rinokosha boka masero, kureva hematopoietic hunde masero. Vane kukwanisa kuwanda uye kusiyanisa kunyika dzakasiyana-siyana inomera hematopoiesis. Imhaka nokuda aumba masero vakura okupedzisira (erythrocytes, leukocytes, maplatelet, etc.). Pasi pokudzora dzinoverengeka nechitarisiko kana dzomukati zvikonzero, zvinotevera sequential kukura chirwere zvigadziriswe:

  • zvishoma nezvishoma kudzikira uwandu hematopoietic hunde masero;
  • Akanetseka Chinangwa chinokosha zvikuru hunde masero kuti kunotoreva hazvibviri inotungamirwa erythrocytes, thrombocytes uye leukocytes;

Kukundwa hunde Sero mune iyi inosimbisa kubudirira mwongo transplantation kubva mapatya kana mukoma / hanzvadzi. saizvozvi ikarapwa aplastic kupererwa neropa mune vana nevakuru. Zvisinei, transplantation hakusi inobudirira kubva kufanana mapatya iri chiitiko kuti mugamuchiri haana kugamuchira pre-kosi zvinodhaka kudzvinyirira zvirwere. Izvi kakawanda akasimbisa masoja yezvakaita chirwere.

The zvikonzero

Zvinosuruvarisa kuti etiological zvikonzero chirwere havasi kuzivikanwa kusvikira pakuguma. Nyanzvi dzinodavira kuti chikonzero chingava:

  • kugara nevanhu mamwe mapoka makemikari;
  • doro;
  • nemagene kubatwa;
  • ionizing nemwaranzi;
  • kudhaka zvinodhaka;
  • zvimwe zvirwere;

Kana vanamazvikokota havagoni kumisa kwainge pamwe zvikonzero dzataurwa pamusoro apa, hosha inonzi idiopathic aplastic kupererwa neropa.

zviratidzo

  • Akacheneruka ganda, kupwanywa.
  • Kupfupika mweya.
  • Inosimudzira muviri tembiricha.
  • Kuneta, kurukutika, dzungu.
  • Tachycardia.
  • Maronda stomatitis.
  • Nasal kana gingival kubuda ropa.
  • Kurasikirwa kudya, kungoerekana uremu.

Izvi handizvo zvose zvekuchipatara zviratidzo sezvo kuonekwe aplastic kupererwa neropa. Zvechokwadi zviratidzo zvisingapindirani nechimwe. Uyezve, kazhinji kufanana nezvimwe zvirwere hematopoietic hurongwa. Ndokusaka zvichikosha kukurumidza kwachiremba uye kuzvipira miedzo yose inodiwa. Kune vamwe mitemo ropa mumwe bonde uye zera. Kana, somuenzaniso, nemakemikari omuviri zviratidzi zvichava siyanei, chiremba akatotanga taurira uwane kuongororwa, uye ipapo zvakakodzera kurapwa.

shepi

Nyanzvi conditionally patsanura mavambo chirwere kupinda mhando mbiri:

1.Vrozhdennaya aplastic kupererwa neropa iri:

  • nhaka (nokurasikirwa neropa inotungamirwa uye vachiberekwa anomalies) Fanconi kupererwa neropa;
  • nhaka (kurasikirwa hematopoiesis pasina vachiberekwa anomalies kukura) kupererwa neropa Oestrich-Dameshek;
  • Mienzaniso dzvuku Sero aplasia (ungaderedza matsvuku eropa count);

2.Priobretennye aplastic kupererwa neropa ndiwo:

  • ane zvachose lesion pamusoro hematopoiesis;
  • pamwe nesarudzo kukundwa erythropoiesis;

Mukuwedzera, maperembudzi Classified maererano zvakaoma kwazvo:

  • Non-zvakakomba aplastic kupererwa neropa. A bvunzo ropa zvinoratidza dzakakwirira kwevari zvimwe vomumatunhu, asi kwete zvakakwana tichienzanisa vasingambooni chakaipa nazvo.
  • Zvakakomba aplastic kupererwa neropa. Underreporting pamusoro maplatelet uye granulocytes ritikulotsitov.

Chii chinosiyanisa Hemorrhagic kupererwa neropa?

Iri zvakajairika mhando kupererwa, kunoitika nokuda ropa rakawanda, zvichitungamirira unopinza kuderera Chizenga muropa, kukura dzinonzi vascular insufficiency uye yakachena nzara. Nokuti zvisingatomboiti akura ngozi yevanhu unovapo panyaya kurasikirwa ropa akapfuudza Vhoriyamu 500 Rine mamiririta.

zvokurwara ichi kazhinji kunoitika kana munhu ectopic pamuviri, ropa kana chiropa chirwere, zvikuru ropa kurasikirwa pashure pakukuvara kana kuvhiyiwa.

Zvinokosha kucherechedza kuti murwere uve kwamazuva mashoma havana chifungidziro kuvapo dambudziko iri. Akazivisa zviratidzo kuoneka mazuva 2-3 mushure kurasikirwa neropa. Kana murwere musingadi zvaaishayiwa unyanzvi, chaizvo mukana rufu.

Dambudziko akadai kupererwa, Hemorrhagic rinorapika. Chiremba anofanira kutanga kubvisa kwainyanya kurasikirwa ropa uye kuwedzerwa kuita colloidal mhinduro.

Diagnostics

Kakawanda vanofungidzirwa hosha kunoitika pashure chokuendesa Analyses preventively. In kupererwa, akaderedza masero matsvuku eropa muropa, ropa masero machena uye Chizenga indices uye ESR siyana zvinoshamisa kwakawedzera. Zvakakosha kuziva kuti ukuru zvinoderedza zviri siyana zvinoriumba dzingasiyana-siyana nomumwe nyaya imwe neimwe.

Kuzosimbisa chirwere aplastic kupererwa, bvunzo ropa haisi nzira chokungorwadzisa nechirwere. Kazhinji chiremba ibasa uwane kuzviongorora murwere, izvo zvinosanganisira:

  • panyama kuongororwa (Kutsunga Ruvara ganda, BP, kuvapo ropa, etc ...);
  • weti kuongorora (kuvapo ropa anoonekwa chiratidzo ane Hemorrhagic chirwere, uye kuvapo tusingaoneki - a kuratidzwa zvinotapukira hunhu yematambudziko);
  • kemesitiri ropa (remafuta akawandisa, shuga, uric acid);
  • apedzise nhoroondo zvokurapa (kana pane tsika dzakaipa, kana paine chirwere, kana kuona zvine chepfu);
  • ropa ongororo;
  • Kudzidza mwongo ponji nzira;
  • electrocardiography;

Chii chinofanira kubatwa?

Chekutanga zvinofanira kucherechedzwa kuti chete nzira dzakakodzera kunogona kubatsira varwere mukurwisa zvirwere zvakadai aplastic kupererwa neropa. Zviratidzo chirwere ichi mu tanga vanofanira kuona munhu wose. Uyezve, kana munhu chikuru zvekuchipatara zviratidzo kunokosha pakarepo kwachiremba nokuda kwemutemo hwakadzama bvunzo.

mushonga Modern inopa zvitatu kuti mushonga. Pasi Kutarira nomumwe zvizere.

  1. Causative kurapwa inokurudzirwa panyaya anozivikanwa kuti kupererwa neropa. Pakadaro, chikuru chinangwa yokurapa ndiko kutungamirira chiito pamusoro afunge chinhu, asi kazhinji isashande. Varwere vari zano kubvisa honzeri chirwere (nokubviswa mapazi nemwaranzi, Kudzimwa mamwe mishonga, etc .. D.). matanho akadaro chete kuderedza mwero rufu mumwongo asi haana kudzorera ropa chakaipa.
  2. Pathogenic kurapwa kunoreva kukura kubvisa chirwere zvigadziriswe. Zvinangwa izvi, vakashandisa immunosuppressive kurapa ( "Cyclophosphamide" zvinodhaka, "Cyclosporin"). Mune zvimwe zviitiko, kushandiswa kwezvinodhaka izvi chinogona chidzosai hematopoietic ushande. It rinoshandiswawo pakurapa corticosteroids uye anabolic steroids. Mishonga izvi hazvifaniri chete zvinowedzera kugadzirwa kweropa masero machena, asiwo kunatsiridza mapuroteni usage. In chakakomba chimiro chirwere, vanachiremba vanokurudzira munhu mwongo nokuisazve. Operation kunyatsoshanda iri yepamusoro zvikuru Varwere vaduku. Aplastic kupererwa neropa muvana uye ikarapwa kuburikidza transplantation.
  3. Symptomatic kurapa inoshandiswa kurwisa chaizvo zvinoratidza chirwere. Rinosanganisira chikuru kuisirwa zvinoumba ropa, asingaurayiwi (mishonga "Fluconazole", "Norfloxacin") uye systemic antifungal kurapa.

Matambudziko uye migumisiro

  • Neta neta pakoma. Nemhaka nokukurumidza kuderera masero matsvuku eropa kuuropi rinenge hapana okisijeni iri kusvitsa, sezvo zvakaita kuti munhu anorasikirwa kuziva uye asingauyi kupindura zviwane.
  • Chirwere.
  • Hemorrhagic yematambudziko (ropa). Kuipa dambudziko - vanonzi Hemorrhagic sitiroko, kana chikamu uropi anofa nokuda impregnate ropa rake.
  • Kushatiswa vamwe zvomukati (kazhinji inoitika pamberi chirwere zvirwere).

Sezvambotaurwa pamusoro akawanda chaizvo vanokwanisa kurapwa zvinobatsira kukunda zvokurwara ichi sezvo aplastic kupererwa neropa. Kufembera kazhinji zvakanaka, asi chete nenguva kurapwa nachiremba. Maererano iripo uwandu, pasina zvakakodzera kurapwa vanenge 90% wevarwere vanofa mukati gore rimwe.

Inonyatsobudirira pakurapa mwongo transplantation rinozivikanwa. Somuenzaniso, 9 pa10 varwere pashure pokuvhiyiwa kurarama anopfuura makore mashanu.

At hazvibviri kuvhiya kupindira (zvinodhaka kurapa) kwemakore anopfuura mashanu anogona makore chete mhenyu hafu varwere, uye kusvika 40.

dziviriro

Primary kudzivirira zvinoreva pedyo chiito kudzivisa nemigumisiro pamusoro siyana zvimwewo zvinoitika. Tiri kutaura pamusoro inokosha kuchengeteka mitoo vari kudyidzana pamwe manyuko ionizing mwaranzi, madhayi. Uyezve, zvinokosha kudzora mishonga uye uwandu husingakuvadzi.

Secondary kudzivirira (kudzivirira Kushatiswa munhu kare kurwara) kunoreva dispensary pakuongorora, uyewo nguva refu yokuzvigadzirisa kurapwa.

Mukugumisa, zvinofanira kucherechedzwa kuti Musatya chirwere chakadai, sezvo aplastic kupererwa neropa. Photos vanhu Vakagwinya vakambova chirwere ichi, kuratidza kuti unogona kugadzirisa dambudziko racho. Muchiitiko chino, basa rinokosha ndohwaJehovha timeliness pokutsvaka hanya unyanzvi uye kunyatsotevedza vanorumbidza zvose kubva vanachiremba. Stay utano!

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