UtanoZvirwere uye Conditions

Tuberous kuoma dzimwe nhengo dzomuviri

Tuberous kuoma dzimwe nhengo dzomuviri - nhaka chirwere, izvo zviri kukonzerwa nokuchinja 16 uye 9 okutodza dzevanhu. Zviratidzo zviri chirwere kuoneka mugore woupenyu achangozvarwa wokutanga. The chirwere kunoratidzwa ganda maronda, ziso, chetsinga kuchinja, anomalies ari zvomukati. Around yepamhino mapundu rinowanika tsvuku panguvo "shavishavi" chimiro uye depigmentatsionnye gwapa, richisvika kuna 1 masendimita ari dhayamita. tuberous
kuoma dzimwe nhengo dzomuviri anoita kuonekwa fibrous plaques pahuma uye anotsvedzerera waxy
growths. Aionekwa sezvo shagreen makwapa - paganda ane ine chisimbiso
pemvura.

Nechepasi yeziso bundu rinenge kuumbwa izvo kanenge growths anochinja ruvara yacho Iris ziso. Tuberous kuoma dzimwe nhengo dzomuviri pane vana kunooneka pacharo muchimiro chinyamunhari chinorwadza anenge pakarepo pashure pokuberekwa. Pfari havaratidzi yakasvikawo, uye pane simba kwazvo. Zvishoma nezvishoma kutanga retardation pfungwa, kusvikira idiocy. Varwere achirwara kuenda kuonana, asingatani autism. Tuberous kuoma dzimwe nhengo dzomuviri hunokonzera panowanikwa polyps uye anomera munzvimbo ura, itsvo, mwoyo uye nezvimwe nhengo dzomukati. Kuvakwa "zinga" chiedza. Kana uchifungidzira kuti chirwere ichi chiri kuitwa resonance yenyukireya uye computed tomography wouropi. yeziso Kuongorora ari kuitwa oftalmografii.

A-siyana kunotoda kurapwa zvinoratidza chirwere dzinokonzerwa kuparadzwa connective uye fibrous zvinyama zviri zvomukati.
Ongororo dzinoratidza kuti mune anomera zvinosanganisira kunyanyisa
uwandu masero mumwe kana mhando dzakawanda. The anorovera zvinogona kukanganisa gyrus
uropi, ivo basal ganglia, brainstem, uye cerebellum. Zvichienderana
localization of bundu kukonzera obstructive hydrocephalus. Nokufamba kwenguva, mashoko anorovera inogona calcined kana kukura musero nyanyisa hofori
astrocytoma. Mune zvisingawanzoitiki Muzviitiko glioblastoma kukura.

Pari, mushonga chirwere hazvigoni saka vakagadzwa chete symptomatic kurapwa. Tuberous kuoma dzimwe nhengo dzomuviri kuri akanzi mu rusvava pa 100,000. Kugwinha yakasvikawo corticosteroids,
Varwere basa nitrazepam uye clonazepam. Kana zvakanangwa kurapwa
nezvipusha retardation kwepfungwa ingava
kumbomira. Tuberous kuoma dzimwe nhengo dzomuviri ikarapwa kushandisa munhu ketogenic kudya pamwe
risinganyanyi makabhohaidhiretsi uye mapuroteni uye yakakwirira - mafuta. izvi zvinoita
zvinogoneka kuti kuderedza kakawanda nezvipusha, uye akabatana kuderedzwa atsetazoplamidom
kuti zvive zvishoma. Kana hydrocephalus shunt rinoitwa. Nokuti rakasungwa ganda rinoitwa argon Laser ganda kururamiswa varwere kuramba ungwaru, izvo kununura ganda growths aesthetic nechinouya. Kana zvinokanganisawo mumapapu akagadzwa progesterone, moyo kubatwa kuchirapa nevamiririri. In zvinoitirwawo renal ropa, zvinouraya nechimbichimbi nephrectomy rinoitwa, hombe renal chikofu phantom.

Matambudziko chokuita mumuviri nomupfungwa nokuremara, zvinofanira kugadziriswa mukutsigira vanhu vakaremara tichibatsirwa chiremba kwepfungwa panguva Center. The inokosha iri mupfungwa rubatsiro
vabereki mwana anorwara. Zvinoitwa kuvarapi, vanachiremba uye vabereki vanofanira kuva
zvainanga nokudzidziswa akazvimiririra chikafu yaunodya, semubereki
utsanana uye kugadzira mwana pachake ari chimbuzi. Tuberous kuoma dzimwe nhengo dzomuviri ane
murombo fungidziro upenyu. Kakawanda, chirwere kumigumo
zvinouraya. Life hunotarisira pamwe chirwere ichi makore anenge 5.

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