UtanoZvirwere uye Conditions

Hemosiderosis chepasi chemapapu: Zviratidzo uye kurapwa

Hemosiderosis chepasi chemapapu - chirwere chakakomba zvikuru. It kunoitika apo vakawanda masero matsvuku eropa neVadzidzi zvinyama womunhu zvemapapu. Kana ichi anopfuurira kwenguva refu kukura hemosiderin ruvara ine simbi.

Chii hemosiderosis?

Rokuongorora chirwere ichi Zvisinei zvinokwanisika chete pahwaro X-ray,, pane zviratidzo zvakawanda iyo kwayo kuvapo inogona vaifungidzira. Zvinoita zviratidzo kuti murwere gemosiderkoz mapapu - a chikosoro zvakaipa, Hawking ropa, kupfupika mweya, ropa mumapapu. Pangave nefivha uye tachycardia.

Pahwaro X-ray chepasi chemapapu chiremba anogona kuita chaicho kuongorora chirwere. dzimwe ongororo vari kuitwawo kusimbisa kuti murwere kutambura kubva chirwere ichi ndicho. Ndicho kuongorora sputum, ropa kemisitiri, mu Muzviitiko zvakaipisisa - zvemapapu biopsy.

Pakurapa chirwere zvinoberekwa kushanda corticosteroids uye zvinodhaka kuti achabvisa chaizvo zviratidzo.

kuratidzwa chirwere

Idiopathic pulmonary hemosiderosis Anonziwo chirwere chinangwa-Gellerstedta. Uyu pathological dambudziko, iyo inoratidza pacharo somugumisiro rinokosha ruvara hemosiderin deposition ari munhu zvemapapu. The chikuru chinoratidza ruvara ichi pakuti inoitwa nedare oxide. Ndiye anokonzera kuchengetera simbi pamuviri. Panguva zvirwere zvakasiyana-siyana zvinoita rinoungana munyama, iyo inotungamirira zvoutano murwere. Uyewo, unogona kuunganidza mumiviri yevanhu.

At paro, hemosiderin - siyana zvakachengetwa mumuviri kupembedza simbi. Nemhaka rejira ichi vane anzi ora Hue. Kana munhu hwapedyo idiopathic pulmonary hemosiderosis, munyama muviri anogona kuunganidza kusvika magiramu shanu dzesimbi.

Roga simbi kuwanda hazvireve kukanganisa kushanda zvinokosha muviri, pane ichi kana zvemapapu. Zvisinei, kana pamwe pulmonary hemosiderosis sclerosis, ari kushanda zvirwere mumuviri hakudzivisiki.

Pangozi varwere kubatwa nechirwere ichi vari vana vaduku uye kuyaruka. Kakawanda kupfuura vakadzi.

Zvinokonzera chirwere

Hemosiderosis chepasi chemapapu anogona kuitika muvanhu nezvikonzero zvakasiyana-siyana. The Zvinonyanyozivikanwa - a vachiberekwa akaremara mudziyo masvingo pulmonary riparadzirwe. Nokuda kwaizvozvi, mumuviri pane kuparadzwa pakati capillaries uye kwenguva kumira ropa kuyerera. Naizvozvo exuded erythrocytes, uye zvemapapu munyama ndivo kakawanda zvemapapu microbleeds.

Somugumisiro simbi iyi anosunungurwa uye muwisira hemosiderin. Iyewo, wefodya nokuda alveolar macrophages uye iiswe epithelia uye masero endothelial yakafarikana mwero. Vakaitawo yenhamo ndero imwe kuremara vachiberekwa. Chakaremara kubatana pakati mitumbi miviri, muchiitiko ichi - the Árbol arteries uye mutsinga yacho yemapapu.

Immunoallergic hunhu chirwere

Zvinokonzera uye morphogenesis pamusoro zvemapapu hemosiderosis kunogonawo immunoallergic. Kana ichi zvirwere zvivako kukonzera kukuvara huru madziro pulmonary capillaries. Pane kutyora wavo wenguva kuvhiyiwa, kuburikidza midziyo mumapapu ukama ropa rikawira zvakawandisa simbi, zvichiita basa muviri zvakakomba anetseka.

Uyewo, kunyanya deposition kuti hemosiderin ari zvemapapu rinenge kunoita kuti nokukurumidza muitiro nokuparadzwa masero matsvuku eropa, aine nokubudiswa Chizenga, kunoitika muna chirwatata. A mukuru azvipire resimbi Absorção de Água ari dumbu, mazhinji kushandisa zvinodhaka rurefu simbi kugutsikana.

Panguva kutanga kwekupwanyiwa pulmonary hemosiderosis muvana munogona somunhu idiopathic chirwere asina chokuita nezvimwe zvinetso. A angaperekedzwa kubudikidza chirwere Gainer (panyaya kana muviri zvakare inonyatsoziva mapuroteni zviri dzinongoitika bovine mukaka).

Kana hemosiderosis kunoitika zvakare, kuti yemapapu mikrokrovotecheniya kungaita kuti chirwere cheBP, iro rinogona kuva chirwere dambudziko.

Uyewo, chirwere angaperekedzwa ari chirwere pamusoro Goodpasture. kukundwa uyu Formação de ari mapapu neitsvo, achiperekedzwa scarring yavo. The chirwere kazhinji pasi varume vane makore 20 kusvika 30 makore. Pane imwe pfungwa pamusoro wayo enhaka hunhu.

mira hemosiderosis

Idiopathic pulmonary hemosiderosis mune vana kazhinji kukonzerwa nezvirwere. Zvinogona kuva nyore SARS, uyewo chirwere chakakomba zvikuru - gwirikwiti, whooping chikosoro uye marariya. Uyewo, kungava nemigumisiro kudhaka.

Mira hemosiderosis ikabuda mwoyo nezvinetso chisingaperi. Zvinogona kuva zvemarudzi ose cardiac chirwere - zvirwere mwoyo, cardio nezvimwe zvirwere.

Zvinogara akadzokorora uye mira hemosiderosis protrude mazhinji kugara yakaderera tembiricha simba mumuviri kana pfungwa kugozha, kushandisa dzimwe mishonga.

Kana hemosiderosis runoyerera mukati Formação de pakati mumapapu, kuti mifananidzo yakajeka anooneka kungoda microbleeds uye nzvimbo nokunyanyisa deposits pakati hemosiderin akafanana nodules, izvo akaronga kubva pakati kusvika arikunze yacho yemapapu.

zviratidzo

Hemosiderosis kunogona kuitika munguva dzakawanda. Chenjera, subacute uye idzokororo. Kana hosha chinoonekwa vana, kazhinji zvinoitika kare kuenda kukireshi zera, kubva pamakore matatu. Zvisinei, pane varwere uyo chirwere rakaiswa vhiki upenyu chokutanga.

Akaratidza chirwere pulmonary ropa uye ropa, kunzwa kufema kukundikana.

Panguva panowanikwa yematambudziko muvanhu rinowanika rinorema chikosoro ruosteessa ruvara, muna Muzviitiko zvakaipisisa, inogona vangakosora ropa. In vana vaduku, ropa kunogona kuva mumarutsi.

On ongororo, vanachiremba ngwarira wheezing, tachycardia, fivha, kazhinji murwere anonyunyuta kurwadziwa muchipfuva uye dumbu, uyewo majoini. Kungavawo zvemamiriro akawedzera chiropa rakapinza ichidonhedzera uremu.

Kana hemoptysis anopfuurira kwenguva refu, murwere hwapedyo kupererwa, simba uye dzungu. The ganda inova rakachenuruka, uye vakakomberedza meso pane maitiro yellowness. Murume ane vaneta nokukurumidza uye anoramba anonzwa ruzha munzeve. Heavy Nguva chirwere chinogona kuitika kubva maawa mashoma mazuva 10-15. Naizvozvo, havagoni kuita ikoko pasina kurapwa.

Panguva achiipa chikosoro uye kupfupika kufema anogona kuderera, asi zvakaoma haana dzinokurudzira, kuona chiremba runodiwa pakarepo. Vari kunyunyuta kuregererwa angasava kuwanikwa zvachose, uye munhu anogona kurarama upenyu huzere shandika.

With nerimwe exacerbation chirwere kuregererwa nguva ipfupi, asi maererano kuwedzera nguva nekuomarara zvinetso. Mumwe migumisiro kupererwa neropa - zvachose Kuparadzwa muviri. Mune zvisingawanzoitiki Muzviitiko, kunyange zvichiita rufu murwere - zvinosiririsa kunogona kuitika nokuda chakasimba pulmonary ropa uye kungoerekana kufema kukundikana.

kuongorora chirwere hemosiderosis

Kuti zvakarurama rokuongorora pulmonary hemosiderosis, unofanira nyanzvi maonero nyanzvi dzinoverengeka. Chokutanga, zviri pulmonologist, hematologist. Uyewo vanofanira kudzidza zvekuchipatara zvinoratidza chirwere. Kuita pasina nokudzidza maekisirei, sputum pachisara ropa (sezvo Kazhinji pachisara uye nokukanganisika) uye zvemapapu biopsy.

Rokuongorora chirwere ichi ndicho zvakaoma. Kazhinji kutora mwedzi kana kunyange kwemakore nyanzvi vasati vanyatsoona chirwere. Dzimwe nguva akamuisa paakanga afa. The ndechokuti chokutanga hachisi chaizvo zviratidzo, kufanana nezvimwe zvirwere zvakawanda, uye vazhinji havana kuvapa ukoshi. Kazhinji chiri kufema chirwere achiperekedzwa chikosoro uye kupererwa neropa.

chenjera danho

Kana vanachiremba chirwere idiopathic pulmonary hemosiderosis, kurapwa zvakakodzera. The muviri pachawo haagoni kurarama dambudziko iri. Mugore chenjera chimiro chirwere achabatsirwa crackles uye palpitations. Panguva iyoyo akaderedza pamwero masero matsvuku eropa, yakakwirira bilirubin siyana pamusoro serum simbi muropa riri shoma.

Panguva nematambudziko kuitika leukocytosis, ESR pamwero rinobuda, izvo kazhinji rinoratidza chokutsva. In akazotevera nzendo chirwere rinowanika polycythemia. Zviri munhu benign nebundu muitiro, achiperekedzwa hyperplasia isiri yekenza kuti mwongo masero.

X-ray zvidzidzo

Kudzidza maekisirei mukutanga nzendo chirwere dzinoratidzwa kuderera pakati pachena kweminda zvemapapu. Panguva iyoyowo, nezuva rechitatu uye chechina nzendo zvinochengetwa zvikuru achiipa uye maronda ose connective zvinyama pamwe noruzhinji mavanga.

Kazhinji kune muzinda mumvuri itsva, pasinei nokuti tsaru kubviswa. On spirography pachena kufema kutambudzika, pamusoro unonzi, electrocardiograph - miokardiostrofiya. Final chirwere kunobatsira zvemapapu biopsy.

hemosiderosis kurapwa

Kunobudirira kurapwa chirwere ichi zvinogoneka chete kana kwenguva refu kurapwa mapoka corticosteroids. Somuenzaniso, "Prednisolone" chinobatsira kurapa pulmonary hemosiderosis. The mushonga waanodzikisira ari permeability midziyo ropa uye kuchititadzisa kukura autoimmune siyana.

Kana kuchinja kurapwa kuzivikanwa kuti basa, ipapo zvomusejari nzira dzinoshandiswa. Anogona zvakazara kana zvishoma akabvisa chirwatata, yekudyidzana izvozvo kunogona kuderedza mukana remissions. Uyewo izvozvo kunoderedza mukana wokuti nematambudziko, uye murwere upenyu hunotarisirwa avhiyiwa ichi achawanda makore 7-10.

Kugadzirira iri rikwanise chokutambudzika chirwere kukura

Zvinokosha kuona kuti mune rikwanise Pasika uye kudzivirira mishonga yakafanana ushandiswe. Apo chirwere kuti "pulmonary hemosiderosis" kurapa maitiro zvinobudirira nokuita mubatanidzwa cytostatic nevamiririri uye plasmapheresis. Izvi zvinoderedza chitarisiko autoantibodies itsva uye kubatsira muviri kukurira tsaru.

Uyewo kubudirira nzira - kubviswa resimbi iri weti, rinoshandiswa kuti aizomupa ichi "Desferal". In pakurapa zviratidzo vakashandisa bronchodilators, antikoagulyarnye zvinoreva.

Long-rokuti kuregererwa vanachiremba vanogona kuzadzisa, apo pamusoro varwere vavo vaitofanira kudya kuti inosiya zvigadzirwa zvose zvakavakirwa mukaka. Kana maperembudzi zvakapinda chirwere danho, zvichida kugadzwa nitrates. zviri kunyanya chokuita mwoyo nematambudziko chisingaperi.

mhando hemosiderosis

Doctors marudzi akasiyana wandei chirwere ichi. Zvikurukuru, pulmonary hemosiderosis inozivikanwa (macropreparations "Brown induration chiedza"). Panyaya iyi, mapapu dzichiwedzera kukura, vane gobvu chaizvo unaku. Uyewo, rima-tsvuku zvisvundu pedyo ari sectional kuoneka whitish rukoko uye brownish inclusions.

Zvinogona kuitika hemosiderosis yemapapu (micropreparations № 111). Muchiitiko chino, shava pigments zvinoonekwa mukati masero uye kunze kuti panguva Murabhoritari maitiro Perls kuva yebhuruu kana greenish. Ivo simuka pakati principales uye Formação de in.

Uyezve, midziyo aya zvemapapu yevanhu wakakurisa zvikuru uye congested. The chirwere achabatsirwa zhinji ropa iri partition pakati Formação de. Panguva iyoyo vari vakaona paiva connective tishu.

Similar articles

 

 

 

 

Trending Now

 

 

 

 

Newest

Copyright © 2018 sn.atomiyme.com. Theme powered by WordPress.