UtanoZvirwere uye Mamiriro

Connes Syndrome: Zvinokonzera, Zviratidzo, uye Zvirwere

Conn's syndrome chirwere chisinganzwisisiki chinosanganiswa nekugadzirwa kwakanyanya kwealdosterone muzvinyorwa zvinonzi adrenal. Somugumisiro wekuwedzera kwehuwandu hwehomoni iyi, pane kusakanganiswa kwekushanda kwehuwandu hwemhepo, hutsika, hutsika uye hutsinye hurumende.

Chirwere chacho chakatanga kurondedzerwa muna 1955. Panguva iyoyo, chiremba anozivikanwa Conne akaongorora chirwere chisingazivikanwi, icho chaifambidzana nehuwandu hwehutachiona hwehutachiona uye kudonha kwemazamu emuviri we potassium. Gare gare zviitiko zvakadaro zvakatsanangurwa navanachiremba kanopfuura kamwechete. Chirwere chacho chakatumidzwa mushure mokutsvakurudza kwekutanga - saka, mumabhuku ekutora akaonekwa chikamu "Kon's syndrome".

Nenzira, kutsvakurudza kwakasimba kwechirwere ichi kuchiri kuitwa nhasi, pamwe nekutsvaga nzira dzakanakisisa dzokurapa nekudzivirira.

Chirwere cheConnie uye chinokonzera

Zvinosuruvarisa, zvikonzero zvekukurudzirwa kwechirwere chakadaro hazvigoni kutsanangurwa nguva dzose. Kunyange zvakadaro, kuvhiringidzika kunowanzoonekwa kwegrenti yakadai kunokonzerwa neAdenoma ye-glomerular zone yezvikamu izvi. Sezvo mutemo, maitiro aya akaoma, saka zviri nyore kubata. Zvakakosha kuziva kuti chirwere chinonyanya kuongororwa pakati pevechidiki, kunyanya pakati pevakadzi.

Kuumbwa uye kupararira kwechirwere kunoenderana nekuwedzera kwealdosterone. Dambudziko rakadaro rinokuvadza mamiriro ehupenyu hwose. Chokutanga, mineral metabolism inoshungurudzwa, zvichiita kuti kuwedzera kuwedzerwa kwe sodium muinalal tubules uye kuwedzerwa kamwechete kwe potassium. Kuderedza kuwanda kwebhatasium mumuviri kunopesana nehutano huri hwetsvo uye chirwere chekufamba.

Connes syndrome: zviratidzo zvechirwere

Kusvika iye zvino, vanachiremba vakaona mapoka matatu ezviratidzo zvikuru zvinoratidzirwa neanorasia, circulatory uye muscular systems.

Chiratidzo chinonyanya kuoneka chechirwere uku kukwirira kweropa, izvo zvinowanzogadziriswa hazvigoni kurarama nehuwandu hwehutachiona. Kuwedzera kunoramba kuwedzera kumanikidzi kunokonzera matambudziko akawanda anowirirana. Varwere vanong'un'una nezvechezzinesi uye musoro, kushaya simba, kushungurudza uye kurutsa. Dzimwe nguva pangave nekurwiswa kwetetany kana kukurudzirwa kwea flaccid kuparara. Kunewo marwadzo mumoyo, nguva dzose kurwiswa kwekushaya simba, kupererwa kwepfufu kana kunyange pane zvishoma zvishoma muviri unoedza. Mumatambudziko akakomba, kukanganiswa kwekoroniyasi kana kwechiremera kunowedzera. Dzimwe nguva hutachiona hwemhepo inobhururuka hunobuda .

Kuwedzera kwekumanikidzwa kunobatawo mamiriro ekuona analyzer - iyo fundus inoshanduka, edema yemagetsi inotaridzika inoonekwa , kuonekwa kwakanaka kunopera (kusvika pakuzadza bofu).

Connes syndrome, sekutonga, inofambidzana nekuwedzera kwehuwandu hwemazuva ose emucheni wakaderedzwa - dzimwe nguva ichi chiyero 10 litita.

Conn's syndrome: kuongororwa uye kurapwa

Mukuvapo kwezvinetso zvakadaro nehutano hwehutano, zvakanakisisa kutsvaga rubatsiro rwechiremba pakarepo. Kuongororwa kwechirwere ndeyekuita kwenguva refu. Kazhinji murwere anofanira kupfuudza urini uye kuongorora ropa. Chiremba anoongororawo uwandu hwe potassium uye aldosterone muropa, inoshandiswa mukuongororwa uye kuverengwa tomography.

Kusvika iye zvino, nzira chete yekurapa kupindira kwekupora. Panguva yekushanda, kana chirwere chinonzi benign kana chikamu che adrenal cortex chibviswa.

Chero zvingava, mushure mekushanda, murwere anofanira kunyatsocherechedza kudya, kuomerera kune mararamiro ane hutano uye kugara achipinda maitiro ekudzivirira.

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