Cruson Syndrome: kliniki yemifananidzo uye kurapa

Cruson Syndrome chirwere chisingawanzoziviki .

General Characteristics

Chirwere chacho chinoratidzwa nehutachiona hwechiso chinowanikwa mukati mekunge intrauterine kukura. Gill arches in embryo yomunhu inoshandiswa pakuchinja, kubva kune zvikamu zvinokosha, kusanganisira maya, zvinozogadzirwa. Kushungurudzika kwekugadzirwa kwemajeri kunotungamirira kune chirwere chinonzi zita rechiremba wechiFrance, uyo akatanga kuritsanangura, Octave Cruson. Ndiye iye akatanga kuona kuti chirwere chacho chiri chechimiro chezvemagetsi: varwere vake vaiva mai nevanasikana. Uyu ndiwo maxillofacial disorder inozivikanwa nehuwandu hwezviratidzo. Zvakasikwa kuti dambudziko riri mumapfupa ehenya: nokuda kwechimwe chikonzero, mwana anogona kuumba zvisina kururama. Semuenzaniso, Cruson's syndrome inogona kuzviratidza mukusanganiswa kwemasopic, coronary kana sagittal suture, kusungurudzwa nguva isati yaitwa ye coronal suture kana yese seams.

Symptomatics

Cruson's syndrome inoratidzirwa nekutumidzwa zviratidzo. Varwere vashoma vanozivikanwa, kupfuura zvose, nehura dzakadzika dzakanyanya. Sezvo mutemo, izvi ndizvo zvinosarudza matambudziko ose ekunzwa anouya munguva yemberi. Muchikamu chikuru kwazvo, chirwere chacho chinoshandurwa kuva chirwere cheMeniere. Pakati pezviratidzo zviratidzo zvinofanira kunziwo brachycephaly, kureva kuti, mutsara mupfupi uye wakapamha, exophthalmos, kureva, maziso anotinhira (izvi zvinotsanangurwa nemakona maduku maduku), hypertelorism, iyo yakareba kure pakati peziso, mhino duku inotaridzika semuromo. Kakawanda, asi kwete zviratidzo zvinotenderwa ndezvomukati uye masaya asina kusimbiswa. Kukura kwakakwana kwemajaya kunotungamirira kukuti chidimbu chinonyatsopfuurira mberi. Zvose izvi zvinosanganisira Cruson syndrome (mifananidzo yevarwere vamunoona munyaya yacho). Nezvikonzero zvisingazivikanwi, varwere vakawanda vane zviuno zvisingaverengeki zvakaderera uye mapepa.

Diagnostics

Sezvo mutemo, pakarepo mushure mekuonekwa kwechecheche, Cruson's syndrome inogona kuongororwa. Zvinokonzera chirwere hazvizivikanwi. Kuti ave nechokwadi chekuvapo kwechirwere, mimwe miedzo ichadiwa: X-rays, magnetic resonance imaging, kuongororwa kwe fundus, maitiro ekuongorora uye kuongorora kwe cerebral cortex.

Frequency

Zvakakosha kuziva kuti chirwere ichi hachina chakanaka: maererano nekuongororwa kwenhamba, kune murwere mumwechete pa 25 000 vanhu vane utano, uye nehupamhi hwehutano iye aive ane vanhu vanotambura nechirwere ichi mumhuri yake.

Kurapa

Nenzira yakawanda, izvo zvinotarisirwa zvinoenderana nekuwanda kwekunyorwa kwetsanga kwakakanganisa hutano hwehupi. Mugore rokutanga rehupenyu, kushandiswa kwekugadzirisa kunogona kuitwa pahenya remuwana. Sezvo mwana ari kukura, maitiro matsva angada kudiwa: pamapfupa, mitsetse, zvinyoro zvishoma zvechiso. Mune zvimwe zviitiko, mushure mekuvhiyiwa, murwere anofanira kupfeka ngowani yakagadzirwa yakagadzirwa. Dambudziko guru nderokuti chirwere ichi chinowanzosangana nekukurumidza muhutano hwekugadzirisa uye kushungurudzika.