Adolph Strümpell Disease: Zviratidzo neMarapirwo

Adolph Strümpell chirwere - a zvokurwara inozivikanwa ne zvishoma nezvishoma kweutera panzvimbo dzapasi maoko nemakumbo, pamwe rakawedzera tsandanyama matauriro mavari. Zviri nhaka chirwere chinogona chirwere chero zera zvachose muduku kusvikira akura kukwegura.

tsananguro

Adolph Strümpell chirwere - chirwere, mberi kusagadzikana tsinga rwevharanda boka heterogeneous zvirwere. It kunoratidzwa vanonzi bilateral lesion of pyramidal turakiti iri Anterior uye posterior musana. Hukuru marudzi chirwere vari yakaumbwa mumakore mashoma okutanga oupenyu, uye recessive - gare gare muupenyu uye akasiyana zvikuru.

Kokutanga zvokurwara ino chinorondedzerwa zvakadzama A. Adolph Strümpell muna 1866. Mazvikokota vati mhuri hunhu chirwere. In mabhuku ezvokurapa pane mamwe mazita zvokurwara (Adolph Strümpell muviri, rwapedyo spastic paraplegia).

Panguva chirwere Inonzi zvishoma nezvishoma. Kuri pana vaduku rinopembererwa zvikuru akaipa hunhu. Kana zvapedzisira kukura neBP uye hyperreflexia kazhinji kuikunda-siyana kufamba zvirwere. The kushurudzira, maererano nenyanzvi, aisimudzira varwere. The mwero kurasikirwa renguva dzose kushanda vanokwanisa anongofunga novimba kwokuomerwa CNS dysfunctions.

Maererano neInternational kupatsanura, Adolph Strümpell chirwere (ICD-10) encoded pasi bumbiro G11.4.

The zvikonzero

Chaiwo zvinokonzera chirwere ichi vari Parizvino zvisingazivikanwi. Avo nounyanzvi chete kutaura hypotheses siyana, asi hapana havasati vawana uchapupu nesayenzi.

nhodzera chirwere

chirwere ichi hunogona kutapukira chete yakatevedzana. Nyanzvi All kuziva dzinoverengeka kwayo mhando:

• Autosomal chikuru (mu vakaroorana apo mumwe vabereki chirwere chirwere ichi, mukana yokuva mwana ane chirwere akadaro pakati 50 uye 100%).
• Autosomal recessive (mukana yokuberekwa ane mwana hako vakaroorana apo mumwe mubereki ari kare kurwara, unogona kuva kubva 0 kusvika 50%).
• Chokuita kuti X chromosome (anowanzodanwa chirwere zvirwere vanhurume).

In okurapa pane chinokosha zviitiko (somuenzaniso, Behr kuti urwere, izvo kunoratidzwa nokuda atrophy of optic etsinga), kana chirwere zviratidzo zviri chaizvo zvakasimba nowenyika rwapedyo spastic paraplegia, asi vari zvakaparadzana zvirwere.

Sezvaratidzwa Adolph Strümpell chirwere? zviratidzo

Kukura chirwere nekuratidzwa zviratidzo zvishoma nezvishoma. Pakutanga varwere vanotsutsumwa okurwadziwa kusanzwa makumbo, kuramba kunzwa kuomarara uye convulsive sunga. Pashure pechinguva yakaoma gumbo flexion ari ibvi mapfundo, saka Kumwe kuchinja kunotanga mhando iyi vari kuwedzera. Vamwe havakwanisi kutora rutsoka kubvisa pasi. Uyezve, zviri akaremara (pfupi uye anova zvishoma kupfuura dzose). In akazotevera matanho pane zvakakomba kutyorwa mashandiro ari pelvic nhengo muchimiro kugara uchida urinate.

marudzi chirwere

Pachishandiswa zviri kuitika zvokurwara, vachitevera zvitarisiko ayo aunonyanya okurapa:

• Nyore (the kunotoda mufananidzo pavarwere koshesa kusimba tsandanyama repasi mapazi pasina concomitant zvirwere).
• Kuoma (kunze yekunwa Zviratidzo Varwere chirwere sezvo malformations womwoyo, rutsoka wakarebesa uye t. D.).

Zvichienderana Kuwanikwa akasimbisa zviitiko chirwere pakati pedyo nehama Munokudzwa:

• chirwere Family Adolph Strümpell (tichiti kuzvitonga kuri mumaruwa kuitwa nevabereki vana).
• Idiopathic shanduro chirwere (iyi, nhoroondo yemhuri zvirwere haina dzakaonekwa).

kuongorora chirwere

Kana uine zviratidzo zvakakosha kwete kuzvicheka-medicate, uye kutsvaka zano zvokurapa. Pamabiko, imwe nyanzvi pakutanga anounganidza nhoroondo murwere zvokurapa, anoteerera zvichemo mibvunzo (apo paiva kusimba makumbo, kana pedyo nehama akafanana zvokurwara uye zvichingodaro. D.).

In danho rinotevera, iri chetsinga kuongorora. Iye zvinoreva nomukuru tinyatsonzwisisa tsandanyama simba maoko nemakumbo, achitsvaga pathological hunenge. Uyezve, anogona kupiwa kombiyuta uye rinobva resonance kuri pamusoro musana pachayo. Kudzidza uku anopa zvikuru zvakawanda kudzidza ayo mamiriro uye kuziva zvinoita rive dete yacho pyramidal maturakiti. Cherechedza kuti kazhinji, CT uye MRI haaratidzi Kumwe kuchinja kunotanga.

Sei munhu anogona kusimbisa chirwere Adolph Strümpell? Chirwere chirwere kunosanganisirawo kudzidza kutsinga dzinouya potentials. Nzira Izvi zvinoita kuti kufungidzira mwero kutsinga dzinouya nomunhu akapoteredza musana. Zviri fanira vanogadzwa kuva DNA bvunzo kuziva pamberi Gene kunotouraya.

With vainyatsotarisirwa vanofanira kuenda differential nechirwere, izvo dzimwe nguva kunokonzera matambudziko. The chirwere kunokosha zvikuru kusiyanisa chirwere Mills - chinopedza lesion zvomusoro tsinga dzinoratidzwa pakuwedzera uropi ventricles uye atrophy pamusoro frontal uye wakakwirira frontal convolution. Akaora, chirwere anoratidza pacharo zvishoma nezvishoma. Mumazuva okupedzisira nzendo chirwere zvinochengetwa bilateral dzomuviri.

Rwapedyo spastic paraplegia kunokosha kusiyanisa pakati vanonzi musana maonero nemultiple sclerosis. Zvakakodzera kufunga mamiriro abdominal hunenge, sphincter, panguva chirwere. Pfungwa iyi nyaya, vakapiwa murwere nhoroondo. Chete pashure kupfuura zvose miedzo uye Muedzo usimbiswe ne Adolph Strümpell chirwere.

mabatiro

Vanobudirira pakurapa chirwere ichi, mushonga ano unogona kupa. Zvipatara ipfupi kutapudzwa zviratidzo uye kuvandudza unhu murwere woupenyu.

Varwere akamuraira mushonga zvishoma nezvishoma rutapudzo kuti tsandanyama matauriro ( "Mydocalm" "Baclofen", "Izoprotan"), mapiritsi ( "Sibazon", "Nozepam", "hlozepida"), mavhitaminzi kuti boka B.

Varwere chirwere ichi zvinoratidza physiotherapy, nemipaini dzokugezera, Paraffin mabhati pamusoro rezasi maoko nemakumbo. Uyezve, migumisiro yakanaka inogona kuonekwa mushure jekiseni, acupressure uye mumuviri kurapa kosi.

Vachibatsira kurapa kunoreva kushandisa chaiyo orthosis, izvo zvinobatsira munhu famba.

Zvakakosha kuziva kuti pane chimwe nechimwe, nzira yokurapa uye vakabatana kurapa vanotumirwa nomumwe. Chiremba anofanira kufunga kwete chete migumisiro yacho muongororo, asi vakawanda mamiriro murwere, kwokuomerwa kurapwa zviratidzo uye kuvapo nezvimwe zvirwere. Kukoshesa kupiwa kusarudza yakarumbidza zvinodhaka uye kuti aashandise mukanyatsochengeta iri akasarudzwa chipimo chemushonga. Zvikasadaro, anowedzera mukana wokuti murombo fungidziro.

Adolph Strümpell chirwere - iri kunzwisisa zvokurwara kubva mupfungwa pfungwa maonero. Uye pedyo nehama vanofanira kupa zvizere kunotsigira. Courses pamusoro symptomatic kurapwa inokurudzirwa kutora kanenge kaviri pagore. With rusingaperi uye zvakakwana vabatwe kuchiita chirwere zvinobvira kumboderera. Izvi zvinoreva kuti munhu anogona kurarama sezvinongoita uye kunyange kushanda kwenguva yakareba.

Matambudziko uye migumisiro

Adolph Strümpell chirwere ngozi kwete chete nokuda kwayo kunotoda mufananidzo. Murume ane chirwere chakadaro tichikufunga kurasikirwa kukwanisa aro zvakazara kufamba pasina rubatsiro. Mukuwedzera, chirwere kunokanganisa basa kwadzakabva ari raidudzwa chetsinga kuremara zvakasikwa sokusava nesimba pamusoro gumbo netsandanyama. Somugumisiro, varwere kungasashanda, zvishoma nezvishoma kufinhwa muupenyu. Saka vanhu vanoda kubatsira kwete chete kune unyanzvi hwakasiyana nenyanzvi, asiwo wepfungwa.

matanho

mushonga Modern havagoni, zvinosuruvarisa zvinopa yakakwana nzira kudzivirira chirwere, rinozivikanwa zvikuru zvikonzero zvayo chidzoke.

Ukuwo, nyanzvi dzinofunga kuti tinofanira kuedza kuramba zvakarurama mararamiro, pakati nepakati inosimbisa, kupa kupfuura zvokudya utano, regai kuputa. Sports firming zvainoita muviri wose. Kana hama vane nhoroondo Adolph Strümpell chirwere, zvinokurudzirwa kuverenga nyaya ino chiremba wako uye, kana zvakakodzera, kanoverengeka gore kupfuura munhu kuongorora zvizere. Wakadaro nzira asingadi yakakodzera chete wanikidza abnormalities, asi kuti kutora matanho ose kuderedza kunoita kwayo.

mhedziso

Munyaya ino, takataura pamusoro chii Adolph Strümpell chirwere. Photo varwere nechirwere ichi kunogona kuwanikwa kushandiswa zvokurapa mabhuku. Chokwadi, zvokurwara ichi haasi chete kunoda unyanzvi pakukurukura kurapwa, asi dzose kunotsigira kubva mhuri.

Masayendisiti pasi pose kuramba vachishingaira kudzidza chirwere ichi, ayo zvinokonzera uye kukura zvakakwana kurapa. Kare, zvave unokosha Gene yaro kunotouraya, izvo zvakananga hunobata pakuonekwa chirwere.

Tinovimba kuti zvose mashoko pano achava kuti chaizvoizvo kubatsira. Stay utano!